Clinical presentation of pheochromocytoma
Pheochromocytoma is uncommon tumor arising form pheochormocytes, the predominant cells of adrenal medulla. The pheochoromocytes constitute the chromaffin system. Pheochromocytoma is most common in the fourth through sixth decades of life. Women and man ara affected with similar frequency. Pheochromocytoma has been called “the 10% tumor” because aproximetaly 10% are bilateral, 10% malignant, 10% occur in children and 10% are extraadrenal/ the extra adrenal lesions are also referad to as paragangliomas.
The presence of pheochromocytoma may provoke fatal hypertensive crises during anesthesia and other stresses.pheochromocytoa are often unrecognized, if 20% of the adult population is hypertensive, only abaout five pheochromocytomas would be expected to be found among 100.000 hypertensives each year. However, about 10% of all pheochromocytomas are found incidentally and out 5% of all incidentalomas are pheochromocytomas. We report a case of a patient presenting with cardiogenic shock due to pheochromocytoma crisis. Treatment of choice is total left adrenalectomy.
Hendari SD, Lefi A
Departement of cardiology and vascular medicine airlangga university
Pheochromocytoma is uncommon tumor arising form pheochormocytes, the predominant cells of adrenal medulla. The pheochoromocytes constitute the chromaffin system. Pheochromocytoma is most common in the fourth through sixth decades of life. Women and man ara affected with similar frequency. Pheochromocytoma has been called “the 10% tumor” because aproximetaly 10% are bilateral, 10% malignant, 10% occur in children and 10% are extraadrenal/ the extra adrenal lesions are also referad to as paragangliomas.
The presence of pheochromocytoma may provoke fatal hypertensive crises during anesthesia and other stresses.pheochromocytoa are often unrecognized, if 20% of the adult population is hypertensive, only abaout five pheochromocytomas would be expected to be found among 100.000 hypertensives each year. However, about 10% of all pheochromocytomas are found incidentally and out 5% of all incidentalomas are pheochromocytomas. We report a case of a patient presenting with cardiogenic shock due to pheochromocytoma crisis. Treatment of choice is total left adrenalectomy.
Hendari SD, Lefi A
Departement of cardiology and vascular medicine airlangga university
